RT Journal Article
SR Electronic
T1 Congenital lymphedema of genitalia and extremities
JF Cleveland Clinic Journal of Medicine
JO Cleve Clin J Med
FD Cleveland Clinic
SP 553
OP 556
VO 51
IS 3
A2 Kenneth J. Tomecki
A1 Jacob W. E. Dijkstra
A1 Wilma F. Bergfeld
A1 Robert Kay
YR 1984
UL http://www.ccjm.org/content/51/3/553.abstract
AB A boy presented at birth with congenital lymphedema of the genitalia. During the following two years, lymphedematous swelling of the right arm and lymphangiectasias, as shown by microscopic examination of noninvolved skin of the other extremities, developed. These generalized lymphatic malformations are rare. The clinical and histopathological changes are detailed, and the possible consequences of furtherdeveloped systematized lymphedema and/or lymphangiosarcoma are discussed. Conservative management, including compression therapy, was ineffective. The initial results of surgical reconstruction were satisfactory.