TABLE 1

Variables used to calculate REVEAL 2.0 risk score

World Health Organization group 1 subgroup
Presence of renal insufficiency
Male age greater than 60
New York Heart Association/World Health Organization functional class
Systolic blood pressure
Heart rate
Six-minute walk test distance
Level of B-type natriuretic peptide
Presence of pericardial effusion
Diffusing capacity of the lung for carbon monoxide on pulmonary function test
Elevated atrial pressures
Any hospitalization within 6 months
Pulmonary vascular resistance
  • REVEAL = Registry to Evaluate Early and Long-Term PAH Disease Management

  • Information from reference 13.