Short communicationStoriform collagenoma (sclerotic fibroma) of the oral mucosa
Introduction
Storiform collagenoma (also called sclerotic fibroma) is uncommon. It occurs as a cutaneous fibrous neoplasm, but appearances at mucosal sites in the head and neck are particularly rare.1, 2, 3 The diagnosis is important, however, as a marker of PTEN hamartoma tumour syndrome or Cowden’s disease, but only when present at multiple sites.4
Section snippets
Case report
A 50-year-old woman presented with 12 months’ history of a slow-growing mass on the hard palate. Clinical examination showed a sessile, firm mass that measured roughly 1 cm in diameter and had normal overlying mucosa. A panoramic radiograph showed no evidence of any abnormality and the presumed diagnosis was a tumour of the minor salivary gland. A computed tomographic (CT) scan showed no erosion or destruction of the bones. Because of the relatively small size of the lesion, we decided to excise
Discussion
Storiform collagenoma or sclerotic fibroma is a benign tumour of the soft tissue, which usually presents as a slowly-enlarging, well-circumscribed mass at cutaneous sites of the face and limbs, although oral mucosal presentations have been published.1 Classically, the histopathological description is of concentrically lamellar patterns or a “plywood-like” arrangement of collagen bundles.5 There are usually positive staining for CD34 and vimentin on immunohistochemical analysis.2
Differential
Conflict of interest
We have no conflicts of interest.
Ethics statement/confirmation of patient’s permission
Ethics approval not required. Verbal consent was obtained for publication but written consent has not been sought as all images are non-identifiable.
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