Kawasaki disease (KD) is an acute self-limiting inflammatory disorder, associated with
vasculitis, affecting predominantly medium-sized arteries, particularly the coronary arteries. In …

Background Different diagnostic and classification criteria are available for hereditary
recurrent fevers (HRF)—familial Mediterranean fever (FMF), tumour necrosis factor receptor-…

<p>Autoinflammatory diseases are characterised by fever and systemic inflammation, with
potentially serious complications. Owing to the rarity of these diseases, evidence-based …

Adenosine deaminases acting on RNA (ADARs) catalyze the hydrolytic deamination of
adenosine to inosine in double-stranded RNA (dsRNA) and thereby potentially alter the …

BACKGROUND. Monogenic IFN–mediated autoinflammatory diseases present in infancy with
systemic inflammation, an IFN response gene signature, inflammatory organ damage, and …

… of Pittsburgh (GA), University of Pittsburgh, PA; Hacettepe University Child Neurology (BA), …
Brogan, PhD … Brogan has received consultancy fees from Roche and Novartis. R. Kneen, G. …

This article proposes a clinical guideline for the diagnosis and treatment of Kawasaki disease
in the UK based on the best available evidence to date, and highlights areas of practice …

Objective To evaluate the genetic findings, demographic features and clinical presentation
of tumour necrosis factor receptor-associated autoinflammatory syndrome (TRAPS) in …

Objective Microparticles are released from endothelial cells in response to a variety of
injurious stimuli and recently have been shown to be increased in a number of diseases …

Objectives To develop a Glucocorticoid Toxicity Index (GTI) to assess glucocorticoid (GC)-related
morbidity and GC-sparing ability of other therapies. Methods Nineteen experts on GC …