Skip to main content

Main menu

  • Home
  • Content
    • Current Issue
    • Ahead of Print
    • Past Issues
    • Supplements
    • Article Type
  • Specialty
    • Articles by Specialty
  • CME/MOC
    • Articles
    • Calendar
  • Info For
    • Manuscript Submission
    • Authors & Reviewers
    • Subscriptions
    • About CCJM
    • Contact Us
    • Media Kit
  • Conversations with Leaders
  • Conference Coverage
    • ACC / WCC 2023
    • AAAAI Meeting 2023
    • ACR Convergence 2022
    • Kidney Week 2022
    • AIDS 2022
    • CHEST 2021
    • IDWeek 2021
    • IAS 2021
    • ADA 2021
    • ATS 2021
    • ACC 2021
    • ACP 2021
    • AAN 2021
  • Other Publications
    • www.clevelandclinic.org

User menu

  • Register
  • Log in

Search

  • Advanced search
Cleveland Clinic Journal of Medicine
  • Other Publications
    • www.clevelandclinic.org
  • Register
  • Log in
Cleveland Clinic Journal of Medicine

Advanced Search

  • Home
  • Content
    • Current Issue
    • Ahead of Print
    • Past Issues
    • Supplements
    • Article Type
  • Specialty
    • Articles by Specialty
  • CME/MOC
    • Articles
    • Calendar
  • Info For
    • Manuscript Submission
    • Authors & Reviewers
    • Subscriptions
    • About CCJM
    • Contact Us
    • Media Kit
  • Conversations with Leaders
  • Conference Coverage
    • ACC / WCC 2023
    • AAAAI Meeting 2023
    • ACR Convergence 2022
    • Kidney Week 2022
    • AIDS 2022
    • CHEST 2021
    • IDWeek 2021
    • IAS 2021
    • ADA 2021
    • ATS 2021
    • ACC 2021
    • ACP 2021
    • AAN 2021
Review

Primary angiitis of the central nervous system: diagnostic criteria and clinical approach

Leonard H. Calabrese, DO, Anthony J. Furlan, MD, Lisa A. Gragg, MS and Trumane J. Ropos, DO
Cleveland Clinic Journal of Medicine May 1992, 59 (3) 293-306;
Leonard H. Calabrese
Department of Rheumatic and Immunologic Disease, The Cleveland Clinic Foundation
  • Find this author on Google Scholar
  • Find this author on PubMed
  • Search for this author on this site
Anthony J. Furlan
Department of Neurology, The Cleveland Clinic Foundation
  • Find this author on Google Scholar
  • Find this author on PubMed
  • Search for this author on this site
Lisa A. Gragg
Department of Biostatistics, The Cleveland Clinic Foundation
  • Find this author on Google Scholar
  • Find this author on PubMed
  • Search for this author on this site
Trumane J. Ropos
Department of Rheumatic and Immunologic Disease, Cleveland Clinic Florida.
  • Find this author on Google Scholar
  • Find this author on PubMed
  • Search for this author on this site
  • Article
  • Info & Metrics
  • PDF
Loading

ABSTRACT

Primary angiitis of the central nervous system has until recently been considered rare, usually progressive, and untreatable. In 1987, preliminary diagnostic criteria for the disorder were proposed in the hope of gaining a more accurate description of the disease. We used these criteria in reviewing all cases reported in the English language (99 cases) and those seen at The Cleveland Clinic Foundation (9 cases). We believe that the disorder is heterogeneous, and has a better prognosis than previously thought. Furthermore, a relatively benign subset of this disorder, termed "benign angiopathy of the central nervous system," can be defined on clinical grounds. We propose a revised set of diagnostic criteria and a practical approach to treatment.

INDEX TERMS
  • Vasculitis
  • Central Nervous System Diseases
  • Copyright © 1992 The Cleveland Clinic Foundation. All Rights Reserved.
PreviousNext
Back to top

In this issue

Cleveland Clinic Journal of Medicine: 59 (3)
Cleveland Clinic Journal of Medicine
Vol. 59, Issue 3
1 May 1992
  • Table of Contents
  • Table of Contents (PDF)
  • Index by author
Download PDF
Article Alerts
Sign In to Email Alerts with your Email Address
Email Article

Thank you for your interest in spreading the word on Cleveland Clinic Journal of Medicine.

NOTE: We only request your email address so that the person you are recommending the page to knows that you wanted them to see it, and that it is not junk mail. We do not capture any email address.

Enter multiple addresses on separate lines or separate them with commas.
Primary angiitis of the central nervous system: diagnostic criteria and clinical approach
(Your Name) has sent you a message from Cleveland Clinic Journal of Medicine
(Your Name) thought you would like to see the Cleveland Clinic Journal of Medicine web site.
CAPTCHA
This question is for testing whether or not you are a human visitor and to prevent automated spam submissions.
Citation Tools
Primary angiitis of the central nervous system: diagnostic criteria and clinical approach
Leonard H. Calabrese, Anthony J. Furlan, Lisa A. Gragg, Trumane J. Ropos
Cleveland Clinic Journal of Medicine May 1992, 59 (3) 293-306;

Citation Manager Formats

  • BibTeX
  • Bookends
  • EasyBib
  • EndNote (tagged)
  • EndNote 8 (xml)
  • Medlars
  • Mendeley
  • Papers
  • RefWorks Tagged
  • Ref Manager
  • RIS
  • Zotero
Share
Primary angiitis of the central nervous system: diagnostic criteria and clinical approach
Leonard H. Calabrese, Anthony J. Furlan, Lisa A. Gragg, Trumane J. Ropos
Cleveland Clinic Journal of Medicine May 1992, 59 (3) 293-306;
Reddit logo Twitter logo Facebook logo Mendeley logo
  • Tweet Widget
  • Facebook Like
  • Linkedin Share Button

Jump to section

  • Article
  • Info & Metrics
  • PDF

Related Articles

  • No related articles found.
  • PubMed
  • Google Scholar

Cited By...

  • Vasculitis on brain angiography is not always vasculitis: intravascular large B-cell lymphoma mimicking central nervous system vasculitis
  • Added Value of Vessel Wall Magnetic Resonance Imaging for Differentiation of Nonocclusive Intracranial Vasculopathies
  • Primary angiitis of the central nervous system: avoiding misdiagnosis and missed diagnosis of a rare disease
  • Cerebral amyloid angiopathy related inflammation: three case reports and a review
  • A rare cause of seizure masquerading as neoplasm
  • Reversible cerebral vasoconstriction syndrome
  • Tumour-like mass lesion: an under-recognised presentation of primary angiitis of the central nervous system
  • A young man with rapidly progressive multifocal disease affecting the white matter
  • Analysis of Central Nervous System Vasculitis with Diffusion-Weighted Imaging and Apparent Diffusion Coefficient Mapping of the Normal-Appearing Brain
  • Nonsystemic vasculitic neuropathy: Insights from a clinical cohort
  • Infectious CNS disease as a differential diagnosis in systemic rheumatic diseases: three case reports and a review of the literature
  • Spinal Cord Involvement in Primary Angiitis of the Central Nervous System: A Report of Two Cases
  • Angiographically defined primary angiitis of the CNS: Is it really benign?
  • CNS Vasculitis in Autoimmune Disease: MR Imaging Findings and Correlation with Angiography
  • Recurrent Intracranial Hemorrhage Due to Postpartum Cerebral Angiopathy : Implications for Management
  • Google Scholar

More in this TOC Section

  • Smallpox and monkeypox: Looking back and looking ahead
  • To repeat or not to repeat? Measuring bone mineral density during anti-resorptive therapy or a drug holiday
  • Colovesical fistula in men with chronic urinary tract infection: A diagnostic challenge
Show more Review

Similar Articles

Keywords

  • VASCULITIS
  • Central Nervous System Diseases

Navigate

  • Current Issue
  • Past Issues
  • Supplements
  • Article Type
  • Specialty
  • CME/MOC Articles
  • CME/MOC Calendar
  • Media Kit

Authors & Reviewers

  • Manuscript Submission
  • Authors & Reviewers
  • Subscriptions
  • About CCJM
  • Contact Us
  • Cleveland Clinic Center for Continuing Education
  • Consult QD

Share your suggestions!

Copyright © 2023 The Cleveland Clinic Foundation. All rights reserved. The information provided is for educational purposes only. Use of this website is subject to the website terms of use and privacy policy. 

Powered by HighWire